Procedure

Total anomalous pulmonary venous connection

Section of Cardiac Surgery, Division of Pediatric Cardiovascular Surgery, University of Michigan School of Medicine, Ann Arbor, MI, USA

^* Corresponding author: ^* F7830, Mott Children's Hospital, 1500 E. Medical Center Drive, Ann Arbor, MI 48109-0223, USA Tel.: +1-734-936 4980; fax: +1-734-763 7353.elbove{at}umich.edu

Total anomalous pulmonary venous connection (TAPVC) is subdivided into four types: supracardiac, cardiac, infracardiac, and mixed. The principle of operative repair is to establish an unobstructed communication between the pulmonary veins and the left atrium, interrupt the connections with the systemic venous circulation, and remove intracardiac shunting. The specific repair is dependent on the type of anomalous connection. Pulmonary venous obstruction is a significant and complex complication following TAPVC repair. The introduction of the sutureless pericardial marsupialization technique has greatly improved the outcome in this difficult patient group.

Key Words: Partial anomalous pulmonary venous connection • Pulmonary venous obstruction • Surgical repair of TAPVC • Total anomalous pulmonary venous connection